Melanotic Neuroectodermal Tumor Presenting as Endolymphatic Sac Tumor
نویسندگان
چکیده
منابع مشابه
Endolymphatic sac tumor
Endolymphatic sac tumor is an uncommon, locally aggressive tumor. The tumor is located in the medial and posterior petrosal bone region and may involve the dura. A hypervascular tumor involving the endolymphatic sac with destructive changes, it involves the bone and may show reactive new bone formation. Diagnosis is based on clinical, radiological, and pathological correlation. We present a cas...
متن کاملEndolymphatic sac tumor.
Endolymphatic sac tumor (ELST) is a papillary epithelial neoplasm arising within the endolymphatic sac/duct that shows a high association with von Hippel-Lindau disease (VHL). There is usually a VHL tumor suppressor gene germline mutation with an autosomal dominant inheritance pattern. Approximately 1 in 35,000 to 40,000 people have VHL, of which approximately 10 to 15% have endolymphatic sac t...
متن کاملMelanotic Neuroectodermal Tumor of Infancy
Melanotic neuroectodermal tumor of infancy (MNETI) is also known as pigmented neuroectodermal tumor of infancy, melanotic prognoma, retinal anlage tumor, pigmented epulis of infancy and congenital melanocarcinoma. It is a rare neoplasm, occuring primarily in maxilla and mandible of infants. Till 1990 about 200 cases had been recorded in world literature(l,2). We report a case with this entity.
متن کاملMelanotic Neuroectodermal Tumor of Infancy
Melanotic neuroectodermal tumor of infancy (MNTI) is a relatively uncommon osteolytic-pigmented neoplasm that primarily affects the jaws of newborn infants. Here, we are reporting a case of MNTI presented at the age of 12 years. The objective of this report is to review the incidence, presentation, investigation protocols, management options and outcomes.
متن کاملMelanotic Neuroectodermal Tumor of Infancy
Melanotic neuroectodermal tumor of infancy (melanotic progonoma) is a rare tumor of neural crest origin that is commonly found in the maxilla of infants (1). Brain involvement is rare (2–4). One report cites malignancy in six cases (1). We describe a case of melanotic neuroectodermal tumor that presented as an aggressive skull-based tumor that was resected and later recurred in the posterior fo...
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ژورنال
عنوان ژورنال: Ear, Nose & Throat Journal
سال: 2019
ISSN: 0145-5613,1942-7522
DOI: 10.1177/0145561319839936